Browsing Trinity College Dublin Theses & Dissertations by Subject "haemophilia B, extended half life, haemophilia outcomes, perioperative outcomes"
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Real-world outcomes with recombinant factor IX Fc fusion protein in people with haemophilia B in Ireland
(Trinity College Dublin. School of Medicine. Discipline of Clinical Medicine, 2023)Haemophilia B is a rare X-linked bleeding disorder resulting from a deficiency of clotting factor IX (FIX), with severe haemophilia B defined as FIX levels < 0.01 IU/mL. Severe haemophilia is characterised by haemarthrosis, ...